Ford, T. J. , Fong, M.W., Cheah, B.C. and Alexopolous, C. (2014) Pulmonary hypertension and hepatic encephalopathy: lethal complications of Rendu-Osler-Weber disease. Journal of the Royal College of Physicians of Edinburgh, 44(2), pp. 126-129. (doi: 10.4997/JRCPE.2014.207) (PMID:24999773)
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Abstract
Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by epistaxis, mucocutaneous telangiectasia with systemic manifestations due to visceral telangiectasia and arterio-venous malformations (AVMs). We describe unusual complications of HHT in a 68-year-old male who developed high-output cardiac failure with pulmonary hypertension in combination with hepatic encephalopathy due to hepatic AVMs. This case shows the importance of a multi-system approach to HHT and considers the treatment of its hepatic complications.
| Item Type: | Articles |
|---|---|
| Status: | Published |
| Refereed: | Yes |
| Glasgow Author(s) Enlighten ID: | Ford, Thomas |
| Authors: | Ford, T. J., Fong, M.W., Cheah, B.C., and Alexopolous, C. |
| College/School: | College of Medical Veterinary and Life Sciences > School of Cardiovascular & Metabolic Health |
| Journal Name: | Journal of the Royal College of Physicians of Edinburgh |
| Publisher: | Royal College of Physicians of Edinburgh |
| ISSN: | 1478-2715 |
| ISSN (Online): | 2042-8189 |
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